Polyarteritis with lung involvement [Churg-Strauss]/EGPA

Churg-Strauss syndrome: Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.

Endpoint definition

Name M13_CHURGSTRAUSS
Long name Polyarteritis with lung involvement [Churg-Strauss]/EGPA
Hospital Discharge registry ICD-10: M301, ICD-9: 4460B
Cause of Death registry ICD-10: M301, ICD-9: 4460B
Level in the ICD-hierarchy 4
First defined in version DF2
Latin name Polyarteritis nodosa cum manifestationibus pulmonalibus

Summary Statistics

Key figures

All Female Male
Number of individuals 44 30 14
Unadjusted prevalence (%) 0.02 0.02 0.01
Mean age at first event (years) 49.88 48.62 52.58
Case fatality at 5-years (%) 4.55 3.33 7.14

Longitudinal metrics

All Female Male
Median nb. of events per indiv. 8.0 8.0 8.0
Recurrence at 6 months (%) 68.18 63.33 78.57

Survival analyses between endpoints

Plot

before Polyarteritis with lung involvement [Churg-Strauss]/EGPA
after Polyarteritis with lung involvement [Churg-Strauss]/EGPA

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Drugs most likely to be purchased after Polyarteritis with lung involvement [Churg-Strauss]/EGPA