Other inherited muscular atrophy

amyotrophic lateral sclerosis: Amyotrophic lateral sclerosis (ALS) is a neurodegenerative disease characterized by progressive muscular paralysis reflecting degeneration of motor neurons in the primary motor cortex, corticospinal tracts, brainstem and spinal cord.

Endpoint definition

Name G6_OTHINMUSC
Long name Other inherited muscular atrophy
Hospital Discharge registry ICD-10: G121, ICD-9: 3351A
Cause of Death registry ICD-10: G121, ICD-9: 3351A
Level in the ICD-hierarchy 3
First defined in version DF2
Latin name Alia atrophia musculorum spinalis congenita

Summary Statistics

Key figures

All Female Male
Number of individuals 20 8 12
Unadjusted prevalence (%) 0.01 0.01 0.01
Mean age at first event (years) 52.06 52.48 51.78
Case fatality at 5-years (%) 10.00 0.00 16.67

Longitudinal metrics

All Female Male
Median nb. of events per indiv. 2.5 1.5 5.0
Recurrence at 6 months (%) 50.00 37.50 58.33

Survival analyses between endpoints

Plot

before Other inherited muscular atrophy
after Other inherited muscular atrophy

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Drugs most likely to be purchased after Other inherited muscular atrophy