Cystic fibrosis, other manifestations/unspecified

obsolete_cystic fibrosis: ['A congenital metabolic disorder affecting the exocrine glands, inherited as an autosomal trait. The secretions of exocrine glands are abnormal, resulting in excessively viscid mucus production which causes obstruction of passageways (including pancreatic and bile ducts, intestines, and bronchi). The sweat sodium and chloride content are increased. Symptoms usually appear in childhood and include meconium ileus, poor growth despite good appetite, malabsorption and foul bulky stools, chronic bronchitis with cough, recurrent pneumonia, bronchiectasis, emphysema, clubbing of the fingers, and salt depletion in hot weather. -- 2003', 'A congenital metabolic disorder affecting the exocrine glands, inherited as an autosomal trait. The secretions of exocrine glands are abnormal, resulting in excessively viscid mucus production which causes obstruction of passageways (including pancreatic and bile ducts, intestines, and bronchi). The sweat sodium and chloride content are increased. Symptoms usually appear in childhood and include meconium ileus, poor growth despite good appetite, malabsorption and foul bulky stools, chronic bronchitis with cough, recurrent pneumonia, bronchiectasis, emphysema, clubbing of the fingers, and salt depletion in hot weather.']

Endpoint definition

Name E4_CYSTFIBRO_NAS
Long name Cystic fibrosis, other manifestations/unspecified
Hospital Discharge registry ICD-10: E849/E848, ICD-8: 2730
Cause of Death registry ICD-10: E848/E849, ICD-8: 2730
Level in the ICD-hierarchy 4
First defined in version DF2

Summary Statistics

Key figures

All Female Male
Number of individuals 23 11 12
Unadjusted prevalence (%) 0.01 0.01 0.01
Mean age at first event (years) 21.10 26.11 16.51
Case fatality at 5-years (%) 0.00 0.00 0.00

Longitudinal metrics

All Female Male
Median nb. of events per indiv. 10.0 17.0 8.0
Recurrence at 6 months (%) 69.57 72.73 66.67

Survival analyses between endpoints

Plot

before Cystic fibrosis, other manifestations/unspecified
after Cystic fibrosis, other manifestations/unspecified

Loading survival analyses plot…

Drugs most likely to be purchased after Cystic fibrosis, other manifestations/unspecified