| Name | D3_IMMUDEFWITHMAJORDEF |
|---|---|
| Long name | Immunodeficiency associated with other major defects |
| Hospital Discharge registry | ICD-10: D82 |
| Cause of Death registry | ICD-10: D82 |
| Include | D3_WISKOTTALDRICH, D3_DIGEORGE, D3_IMMUDEFSHORTLIMB, D3_IMMUDEFPOSTEBV, D3_HYPERIGESDR, D3_IMMUDEFMAJORDEFNAS |
| Level in the ICD-hierarchy | 3 |
| First defined in version | DF2 |
| Latin name | Deficientia immunalis cum aliis defectibus majoribus |
| All | Female | Male | |
|---|---|---|---|
| Number of individuals | 36 | 19 | 17 |
| Unadjusted prevalence (%) | 0.02 | 0.02 | 0.02 |
| Mean age at first event (years) | 41.41 | 45.95 | 36.35 |
| Case fatality at 5-years (%) | 5.56 | 5.26 | 5.88 |
| All | Female | Male | |
|---|---|---|---|
| Median nb. of events per indiv. | 2.5 | 3.0 | 2.0 |
| Recurrence at 6 months (%) | 52.78 | 47.37 | 58.82 |
before Immunodeficiency associated with other major defects
after Immunodeficiency associated with other major defects
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