congenital nonspherocytic hemolytic anemia: Any one of a group of congenital hemolytic anemias in which there is no abnormal hemoglobin or spherocytosis and in which there is a defect of glycolysis in the erythrocyte. In some cases, pyruvate kinase deficiency has been demonstrated; in other cases, glucose-6-phosphate dehydrogenase deficiency has been demonstrated.
| Name | D3_ANAEMIAENZYME |
|---|---|
| Long name | Anaemia due to enzyme disorders |
| Hospital Discharge registry | ICD-10: D55, ICD-8: 282[2-3] |
| Cause of Death registry | ICD-10: D55, ICD-8: 282[2-3] |
| Level in the ICD-hierarchy | 3 |
| First defined in version | DF2 |
| Latin name | Anaemiae ex perturbationibus enzymaticis |
| All | Female | Male | |
|---|---|---|---|
| Number of individuals | 9 | - | - |
| Unadjusted prevalence (%) | 0.00 | - | - |
| Mean age at first event (years) | 31.49 | - | - |
| Case fatality at 5-years (%) | 11.11 | - | - |
| All | Female | Male | |
|---|---|---|---|
| Median nb. of events per indiv. | 1.0 | - | - |
| Recurrence at 6 months (%) | 44.44 | - | - |
before Anaemia due to enzyme disorders
after Anaemia due to enzyme disorders
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