systemic scleroderma: A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. The two types of systemic scleroderma, limited cutaneous and diffuse cutaneous are classified with focus on the extent of affected skin. A relationship exists between the extent of skin area affected and degree of internal organ/system involvement. Systemic scleroderma can manifest itself in pulmonary fibrosis, Raynaud's syndrome, digestive system telangiectasias, renal hypertension and/or pulmonary hypertension.
| Name | M13_SYSTSLCE |
|---|---|
| Long name | Systemic sclerosis |
| Hospital Discharge registry | ICD-10: M34, ICD-8: 7340 |
| Cause of Death registry | ICD-10: M34, ICD-8: 7340 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
| Latin name | Sclerosis systemica |
| All | Female | Male | |
|---|---|---|---|
| Number of individuals | 302 | 251 | 51 |
| Unadjusted prevalence (%) | 0.14 | 0.20 | 0.05 |
| Mean age at first event (years) | 53.68 | 54.06 | 51.85 |
| Case fatality at 5-years (%) | 5.63 | 4.38 | 11.76 |
| All | Female | Male | |
|---|---|---|---|
| Median nb. of events per indiv. | 5.0 | 5.0 | 2.0 |
| Recurrence at 6 months (%) | 71.19 | 74.90 | 52.94 |
before Systemic sclerosis
after Systemic sclerosis
Loading survival analyses plot…
Loading survival analyses table…