obsolete_Job's syndrome: ['Primary immunodeficiency syndrome characterized by recurrent infections and hyperimmunoglobulinemia E. Most cases are sporadic. Of the rare familial forms, the dominantly inherited subtype has additional connective tissue, dental and skeletal involvement that the recessive type does not share.']
| Name | D3_HYPERIGESDR |
|---|---|
| Long name | Hyperimmunoglobulin E [IgE] syndrome |
| Hospital Discharge registry | ICD-10: D824 |
| Cause of Death registry | ICD-10: D824 |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
| Latin name | Syndroma hyperimmunoglobulini E (IgE) |
| All | Female | Male | |
|---|---|---|---|
| Number of individuals | 7 | - | - |
| Unadjusted prevalence (%) | 0.00 | - | - |
| Mean age at first event (years) | 43.62 | - | - |
| Case fatality at 5-years (%) | 14.29 | - | - |
| All | Female | Male | |
|---|---|---|---|
| Median nb. of events per indiv. | 13.0 | - | - |
| Recurrence at 6 months (%) | 85.71 | - | - |
before Hyperimmunoglobulin E [IgE] syndrome
after Hyperimmunoglobulin E [IgE] syndrome
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